Search on: PORPHOBILINOGEN SYNTHASE 
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Descriptor English:   Porphobilinogen Synthase 
Descriptor Spanish:   Porfobilinógeno Sintasa 
Descriptor Portuguese:   Sintase do Porfobilinogênio 
Synonyms English:   ALA Dehydrase
ALA-Dehydrase
Acid Dehydratase, Aminolevulinic
Acid Dehydratase, delta-Aminolevulinic
Aminolevulinate Hydro Lyase
Aminolevulinate Hydro-Lyase
Aminolevulinic Acid Dehydratase
Dehydratase, Aminolevulinic Acid
Dehydratase, delta-Aminolevulinate
Dehydratase, delta-Aminolevulinic Acid
Hydro-Lyase, Aminolevulinate
Synthase, Porphobilinogen
delta Aminolevulinate Dehydratase
delta Aminolevulinic Acid Dehydratase
delta-Aminolevulinate Dehydratase
delta-Aminolevulinic Acid Dehydratase  
Tree Number:   D08.811.520.241.300.550
Definition English:   An enzyme that catalyzes the formation of porphobilinogen from two molecules of 5-aminolevulinic acid. EC 4.2.1.24. 
History Note English:   98(73) 
Allowable Qualifiers English:  
AD administration & dosage AE adverse effects
AN analysis AI antagonists & inhibitors
BI biosynthesis BL blood
CF cerebrospinal fluid CS chemical synthesis
CH chemistry CL classification
DF deficiency DE drug effects
EC economics GE genetics
HI history IM immunology
IP isolation & purification ME metabolism
PK pharmacokinetics PD pharmacology
PH physiology PO poisoning
RE radiation effects ST standards
SD supply & distribution TU therapeutic use
TO toxicity UL ultrastructure
UR urine  
Record Number:   633 
Unique Identifier:   D000623 

Occurrence in VHL:
 

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